ICD-10-CM · E00–E89Billable

ICD-10-CM Code E78.019

Familial hypercholesterolemia, unspecified

Source: CMS ICD-10-CM FY2026Effective Reviewed by the D3rx Clinical Billing Team

Diagnosis information

Billable

Yes

Valid for claim submission

Chapter

E00–E89

Endocrine, nutritional and metabolic diseases

Risk adjustment

None

Not risk-adjustable (V28)

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More codes in the E78 category

Other billable ICD-10-CM codes in the same category as E78.019. Coding to the highest specificity the documentation supports is what keeps a claim clean — pick the child code that most precisely matches the diagnosis.

  • E78.00Pure hypercholesterolemia, unspecified
  • E78.010Homozygous familial hypercholesterolemia [HoFH]
  • E78.011Heterozygous familial hypercholesterolemia [HeFH]
  • E78.1Pure hyperglyceridemia
  • E78.2Mixed hyperlipidemia
  • E78.3Hyperchylomicronemia
  • E78.41Elevated Lipoprotein(a)
  • E78.49Other hyperlipidemia
  • E78.5Hyperlipidemia, unspecified
  • E78.6Lipoprotein deficiency
  • E78.70Disorder of bile acid and cholesterol metabolism, unspecified
  • E78.71Barth syndrome

Documentation & coding notes

  • E78.019 is a billable/specific ICD-10-CM code — it can be reported as a primary or secondary diagnosis when the documentation supports it. Code to the highest level of specificity the record allows.
  • Always verify the code against the current ICD-10-CM Official Guidelines and the payer's coverage policy before submitting — coverage, medical necessity edits, and sequencing rules vary by payer.

Related E00–E89 codes

Questions about coding E78.019?

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Medical coding disclaimer

ICD-10-CM codes and descriptions shown are from the CMS FY2026 official code set and HCC mappings from the CMS-HCC V28 model (payment year 2026), shown for educational reference. Official Guidelines, payer coverage, medical-necessity edits, and sequencing rules vary. Always verify with the current ICD-10-CM Official Guidelines and the payer before submitting claims. D3rx is not responsible for coding or billing outcomes.